familiaire aandoening	genetische aandoening	letsel van digitus van hand, exclusief digitus I	letsel van gewricht	osteonecrose van digitus van hand	structurele afwijking van epifyse van falanx van hand	structurele afwijking van interfalangeaal gewricht van hand	zwelling van gewricht van digitus van hand, exclusief digitus I
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familiaire osteoartropathie van digiti van hand, exclusief digitus I (aandoening)
	familiaire osteoartropathie van digiti van hand, exclusief digitus I
	familiale osteoartropathie van vingers
	Thiemann disease familial form
	Familial osteoarthropathy of fingers Thiemann's disease Thiemann syndrome Osteochondrosis of phalangeal epiphyses Aseptic necrosis of phalangeal epiphyses
	A very rare genetic necrotic bone disorder with clinical characteristics of painless swelling of the proximal interphalangeal joints associated with osteonecrosis of epiphyses followed by osteoarthritic changes, with onset before 25 years of age and often a benign course.

Id	55166000
Status	Primitive

Associated morphology	zwelling
Finding site	structuur van proximaal interfalangeaal gewricht van digitus van hand, exclusief digitus I

Associated morphology	avasculaire necrose
Finding site	structuur van epifyse van falanx van digitus van hand, exclusief digitus I

DHD Diagnosis thesaurus reference set

RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set

Target	M87.04
Term	Idiopathische aseptische botnecrose van hand

SNOMED CT to Orphanet simple map

3314

SNOMED CT to ICD-10 extended map

Target	M87.04
Rule	TRUE
Advice	ALWAYS M87.04
Correlation	SNOMED CT source code to target map code correlation not specified