| Thiemann disease familial form (disorder) | | Thiemann disease familial form | | Familial osteoarthropathy of fingers
Thiemann's disease
Thiemann syndrome
Osteochondrosis of phalangeal epiphyses
Aseptic necrosis of phalangeal epiphyses
| | A very rare genetic necrotic bone disorder with clinical characteristics of painless swelling of the proximal interphalangeal joints associated with osteonecrosis of epiphyses followed by osteoarthritic changes, with onset before 25 years of age and often a benign course. |
| | Id | 55166000 | | Status | Primitive |
| SNOMED CT to Orphanet simple map |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | M87.04 | | Term | Idiopathische aseptische botnecrose van hand |
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| SNOMED CT to ICD-10 extended map | | Target | M87.04 | | Rule | TRUE | | Advice | ALWAYS M87.04 | | Correlation | SNOMED CT source code to target map code correlation not specified |
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