| congenitale gegeneraliseerde lipodystrofie (aandoening) | | congenitale gegeneraliseerde lipodystrofie | | syndroom van Berardinelli-Seip congenitale totale lipodystrofie Berardinelli-Seip-syndroom
|  | Dit betekent dat je over je hele lichaam weinig of geen vet onder je huid hebt. Je bent hiermee geboren. | | Congenital generalized lipodystrophy | | Congenital total lipodystrophy Seip's syndrome Beradinelli-Seip syndrome Total lipoatrophy Lawrence-Seip syndrome Berardinelli's syndrome Lipoatrophic diabetes mellitus Berardinelli-Seip congenital lipodystrophy
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| | Id | 284449005 | | Status | Primitive |
| DHD Diagnosis thesaurus reference set |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | E88.1 | | Term | Lipodystrofie, niet elders geclassificeerd |
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| SNOMED CT to ICD-10 extended map | | Target | E88.1 | | Rule | TRUE | | Advice | ALWAYS E88.1 | POSSIBLE REQUIREMENT FOR AN EXTERNAL CAUSE CODE | | Correlation | SNOMED CT source code to target map code correlation not specified |
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