| Triglyceride deposit cardiomyovasculopathy (disorder) | | Triglyceride deposit cardiomyovasculopathy | | TGCV - triglyceride deposit cardiomyovasculopathy Neutral lipid storage disease with severe cardiovascular involvement
| | A rare cardiovascular disorder characterised by defective intracellular lipolysis of long-chain triglycerides (LCTG), resulting in heart failure and diffuse atherosclerosis. |
| | Id | 1373754008 | | Status | Primitive |
| SNOMED CT to ICD-10 extended map | | Target | E78.8 | | Rule | TRUE | | Advice | ALWAYS E78.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | | Correlation | SNOMED CT source code to target map code correlation not specified |
| Target | I43.1 | | Rule | TRUE | | Advice | ALWAYS I43.1 | THIS CODE MAY BE USED IN THE PRIMARY POSITION WHEN THE MANIFESTATION IS THE PRIMARY FOCUS OF CARE | | Correlation | SNOMED CT source code to target map code correlation not specified |
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