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Paraneoplastic isolated brainstem encephalitis (disorder)
Paraneoplastic isolated brainstem encephalitis
Paraneoplastic isolated rhomboencephalitis
Paraneoplastic isolated rhombencephalitis
A rare autoimmune encephalitis characterized by various phenotypes depending on the region of the brainstem that is involved; patients present with gaze palsies (in midbrain involvement), facial palsy or vertical gaze palsies (in pontine involvement), dysarthria, dysphagia or central hypoventilation (in medullary involvement). Additional clinical features may also involve pyramidal symptoms and gait impairment.
Id1365681000
StatusPrimitive
Due toneoplasma
Associated morphologyinflammatoire morfologie
Finding sitestructuur van truncus encephali
Pathological processauto-immuunproces
Associated morphologyinflammatoire morfologie
Finding sitestructuur van weefsel van hersenen
Pathological processauto-immuunproces
SNOMED CT to ICD-10 extended map
TargetG04.8
RuleTRUE
AdviceALWAYS G04.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified