folliculair T-cellymfoom
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Nodal T-follicular helper cell lymphoma follicular type (disorder)
Nodal T-follicular helper cell lymphoma follicular type
nTFHL-F - nodal T-follicular helper cell lymphoma follicular type
Follicular helper T-cell lymphoma, follicular type
Nodal T-cell lymphoma with TFH phenotype
A rare T-cell non-Hodgkin lymphoma characterized by generalized lymphadenopathy and predominantly follicular or perifollicular growth pattern, consistent with the expression of T-follicular helper markers. Affected individuals distinctly lack histologic features (such as proliferation of high endothelial venules and expanded follicular dendritic meshworks) typically associated to angioimmunoblastic T-cell lymphoma. It affects elderly individuals (mostly at the sixth decade of life) that present with advanced-stage disease. Majority of the cases have disseminated nodal involvement, whereas involvement of extranodal sites including skin, liver, spleen and bone marrow are also reported. Patients may therefore develop skin rash and immune manifestations.
Id1362026000
StatusPrimitive
Associated morphologyfolliculair T-cellymfoom
SNOMED CT to ICD-10 extended map
TargetC82.7
RuleTRUE
AdviceALWAYS C82.7 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified