ziekte van von Willebrand type 3 (aandoening) | | ziekte van von Willebrand type 3 | | Hereditary von Willebrand disease type 3 | | von Willebrand disease type III von Willebrand disease type 3
| | A form of von Willebrand disease (VWD) characterized by a bleeding disorder associated with a total or near-total absence of Willebrand factor (VWF) in the plasma and cellular compartments, also leading to a profound deficiency of plasmatic factor VIII (FVIII). It is the most severe form of VWD. |
| Id | 128108002 | Status | Primitive |
DHD Diagnosis thesaurus reference set |
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | Target | D68.0 | Term | Ziekte van Willebrand |
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SNOMED CT to Orphanet simple map | 166096 |
SNOMED CT to ICD-10 extended map | Target | D68.0 | Rule | TRUE | Advice | ALWAYS D68.0 | Correlation | SNOMED CT source code to target map code correlation not specified |
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