| familiair neuro-endocrien neoplasma gastrisch type 1 (aandoening) | | familiair neuro-endocrien neoplasma gastrisch type 1 | | familiaire neuro-endocriene tumor gastrisch type 1
| | Familial gastric type 1 neuroendocrine neoplasm | | Familial gastric type 1 neuroendocrine tumor
| | A rare neoplastic disease characterized by occurrence of atypical and aggressive gastric type 1 neuroendocrine tumors (NET) in early adulthood. The tumors often show nodal infiltration requiring total gastrectomy. Synchronous gastric adenocarcinoma has also been reported. Patients present high serum gastrin concentrations and iron-deficiency anemia rather than megaloblastic anemia, which is a typical feature in patients with sporadic gastric type 1 NET where the tumor usually arises on the background of autoimmune atrophic gastritis. |
| | Id | 1264340007 | | Status | Primitive |
| SNOMED CT to Orphanet simple map | 464756 |
| SNOMED CT to ICD-10 extended map | | Target | C16.9 | | Rule | TRUE | | Advice | ALWAYS C16.9 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | | Correlation | SNOMED CT source code to target map code correlation not specified |
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