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immunoglobuline G4-gerelateerde aandoening van glandula submandibularis (aandoening)
immunoglobuline G4-gerelateerde aandoening van glandula submandibularis
IgG4-gerelateerde aandoening van onderkaakspeekselklier
IgG4-gerelateerde aandoening van submandibulaire klier
Küttner-tumor
Immunoglobulin G4 related submandibular gland disease
IgG4-related submandibular gland disease
Küttner tumor
A rare disease characterized by a benign tumor-like chronic inflammatory lesion of the submandibular gland. Histologic features are periductal fibrosis, acinar atrophy, obliterative phlebitis, dense lymphoplasmacytic infiltrates rich in IgG4-positive plasma cells and formation of lymphoid follicles. Lobular architecture is preserved. Patients most commonly present with unilateral, painless swelling of the submandibular gland. Serologic analysis reveals elevated IgG4 levels.
Id1264005000
StatusPrimitive
SNOMED CT to Orphanet simple map449432
SNOMED CT to ICD-10 extended map
TargetK11.2
RuleTRUE
AdviceALWAYS K11.2 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified