lymfoplasmocytair lymfoom
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lymfoplasmacytair lymfoom zonder productie van immunoglobuline M (aandoening)
lymfoplasmacytair lymfoom zonder productie van immunoglobuline M
lymfoplasmacytisch lymfoom zonder immunoglobuline-M-productie
lymfoplasmocytair lymfoom zonder IgM-productie
Lymphoplasmacytic lymphoma without immunoglobulin M production
Lymphoplasmacytic lymphoma without IgM (immunoglobulin M) production
Lymphoplasmacytic lymphoma without IgM production
A rare B-cell non-Hodgkin lymphoma characterized by the presence of small B-lymphocytes, plasmacytoid lymphocytes and plasma cells, and either non-secreting or secreting IgG or IgA paraproteins. The disease usually involves the bone marrow and sometimes also the spleen or lymph nodes. Patients typically present with symptoms related to anemia. Hyperviscosity, autoimmune phenomena and B symptoms may also be observed. Mortality is higher as compared to Waldenström macroglobulinemia.
Id1255270006
StatusPrimitive
Associated morphologylymfoplasmocytair lymfoom
SNOMED CT to Orphanet simple map443159
SNOMED CT to ICD-10 extended map
TargetC83.0
RuleTRUE
AdviceALWAYS C83.0 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified