| | deficiëntie van 3-hydroxyacyl-co-enzym-A-dehydrogenase (aandoening) |  |  | deficiëntie van 3-hydroxyacyl-co-enzym-A-dehydrogenase |  |  | deficiëntie van 3-hydroxyacyl-CoA-dehydrogenase
 |  |  | Dit betekent dat je lichaam bepaalde vetten niet goed kan afbreken. Deze vetten hopen zich op in je cellen. Daardoor werken je cellen steeds slechter. |  |  | Deficiency of 3-hydroxyacyl-CoA dehydrogenase |  |  | Deficiency of beta-hydroxyacyl dehydrogenaseDeficiency of beta-keto-reductase
 
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 | | Id | 124122005 |  | Status | Primitive | 
| DHD Diagnosis thesaurus reference set | 
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set |  | | Target | E71.3 |  | Term | Stoornissen van vetzuurmetabolisme | 
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| SNOMED CT to Orphanet simple map | 309127 | 
| SNOMED CT to ICD-10 extended map |  | | Target | E71.3 |  | Rule | TRUE |  | Advice | ALWAYS E71.3 | POSSIBLE REQUIREMENT FOR AN EXTERNAL CAUSE CODE |  | Correlation | SNOMED CT source code to target map code correlation not specified | 
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