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idiopathische ductopenie (aandoening)
idiopathische ductopenie
Idiopathic ductopenia
Idiopathic adult ductopenia
IAD - idiopathic adult ductopenia
A rare biliary tract disease with characteristics of loss of interlobular bile ducts resulting in chronic cholestasis, without any known cause. Loss of less than 50% of interlobular bile ducts is associated with a mild disease course, while loss of the majority of ducts results in a severe form, potentially leading to cirrhosis and liver failure. Patients typically present as young or middle-aged adults with episodic jaundice, pruritus and elevated liver enzymes.
Id1234822009
StatusPrimitive
Clinical coursechronisch
SNOMED CT to Orphanet simple map480512
SNOMED CT to ICD-10 extended map
TargetK83.8
RuleTRUE
AdviceALWAYS K83.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION
CorrelationSNOMED CT source code to target map code correlation not specified