'smoldering' systemische mastocytose (aandoening) | | 'smoldering' systemische mastocytose | | 'smouldering' systemische mastocytose
| | Smoldering systemic mastocytosis | | SSM - smoldering systemic mastocytosis
| | A rare, slowly progressive form of systemic mastocytosis (SM) characterized by gradual accumulation of neoplastic mast cells in the visceral organs. Patients typically present with splenomegaly, hypercellular marrow and, in most cases, urticaria pigmentosa-like skin lesions. |
| Id | 1231732006 | Status | Defined |
DHD Diagnosis thesaurus reference set |
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | Target | D47.0 | Term | Tumoren van histiocyten en mestcellen met onzeker of onbekend gedrag |
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SNOMED CT to Orphanet simple map | 158775 |
SNOMED CT to ICD-10 extended map | Target | C96.2 | Rule | TRUE | Advice | ALWAYS C96.2 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | Correlation | SNOMED CT source code to target map code correlation not specified |
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