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Papillary intralymphatic angioendothelioma (disorder)
Papillary intralymphatic angioendothelioma
Primary intralymphatic angioendothelioma
Dabska tumor
Endovascular papillary angioendothelioma
A rare vascular tumor characterized by an ill-defined, slowly growing, asymptomatic cutaneous plaque or nodule mostly involving the limbs, in fewer cases the trunk. The tumor is composed of lymphatic-like channels with prominent intraluminal papillary tufts with hyaline cores lined by hobnail endothelial cells. It is locally aggressive, while metastasis is rare. Infants and children are much more often affected than adults.
Id1231180000
StatusDefined
ICD-10 complex map reference set
TargetD48.1
RuleTRUE
AdviceALWAYS D48.1 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified
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