maligne epitheliaal neoplasma
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'nuclear protein in testis'-geassocieerd carcinoom (aandoening)
'nuclear protein in testis'-geassocieerd carcinoom
NUT-geassocieerd carcinoom
NUT (nuclear protein in testis) carcinoma
NUT (nuclear protein in testis) midline carcinoma
Nuclear protein in testis carcinoma
A rare tumor characterized by a rapidly growing mass usually arising along the midline, defined by the presence of NUTM1 rearrangements. Histopathological examination shows a poorly differentiated carcinoma, often with evidence of squamous differentiation. Patients present with unspecific signs and symptoms due to mass effect depending on the location. Extensive local invasion of adjacent structures, lymph node involvement and distant metastatic disease are often present at the time of diagnosis. Prognosis is generally poor.
Id1187622004
StatusDefined
Associated morphology'nuclear protein in testis'-geassocieerd carcinoom
SNOMED CT to Orphanet simple map443167
SNOMED CT to ICD-10 extended map
TargetC80.9
RuleTRUE
AdviceALWAYS C80.9 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified