| syndroom van trombocytopenie, anasarca, koorts, nierinsufficiëntie en organomegalie (aandoening) | | syndroom van trombocytopenie, anasarca, koorts, nierinsufficiëntie en organomegalie | | TAFRO-syndroom
syndroom van trombopenie, gegeneraliseerd oedeem, pyrexie, nierschade en splanchnomegalie
syndroom van trombopenie, gegeneraliseerd oedeem, febris, nierschade en visceromegalie
| | TAFRO syndrome | | TAFRO (thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly) syndrome
Thrombocytopenia, anasarca, fever, renal insufficiency, organomegaly syndrome
| | A rare systemic disease characterized by acute or subacute onset of thrombocytopenia, anasarca (edema, pleural effusion, ascites) and systemic inflammation (fever and/or elevated C-reactive protein). Minor diagnostic categories are Castleman disease-like features on lymph node biopsy, reticulin myelofibrosis and/or increased number of megakaryocytes in bone marrow, progressive renal insufficiency and mild organomegaly including hepatosplenomegaly and lymphadenopathy. Most patients show elevated levels of serum alkaline phosphatase while marked polyclonal hypergammopathy is rare. |
| | Id | 1187615007 | | Status | Primitive |
| SNOMED CT to Orphanet simple map | 457077 |
| SNOMED CT to ICD-10 extended map | | Target | M35.8 | | Rule | TRUE | | Advice | ALWAYS M35.8 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | | Correlation | SNOMED CT source code to target map code correlation not specified |
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