| immunoglobuline G4-gerelateerde oftalmopathie (aandoening) | | IgG4-gerelateerde oftalmopathie | | immunoglobuline G4-gerelateerde oftalmopathie
IgG4-gerelateerde oogaandoening
| | Immunoglobulin G4 related ophthalmic disease | | IgG4 (immunoglobulin G4) related ophthalmic disease
| | A rare inflammatory eye disease with characteristics of IgG4 (immunoglobulin G4) immunopositive lymphocyte and plasmacyte infiltration and collagenous fibrosis of affected tissue and elevated serum levels of IgG4. Clinical presentation includes mass lesion or swelling of the involved structures, commonly involving lacrimal gland and duct, infraorbital and supraorbital nerves, extraocular muscles and orbital soft tissues. A systemic involvement is common. |
| | Id | 1187510006 | | Status | Primitive |
| DHD Diagnosis thesaurus reference set |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | D89.8 | | Term | Overige gespecificeerde aandoeningen waarbij immuunsysteem betrokken is, niet elders geclassificeerd |
| Target | H57.9 | | Term | Aandoening van oog en adnexen, niet gespecificeerd |
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| SNOMED CT to Orphanet simple map | 449563 |
| SNOMED CT to ICD-10 extended map | | Target | H05.1 | | Rule | TRUE | | Advice | ALWAYS H05.1 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | | Correlation | SNOMED CT source code to target map code correlation not specified |
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