| hooggradig B-cellymfoom met herschikking van MYC, BCL2 en/of BCL6 (aandoening) | | hooggradig B-cellymfoom met herschikking van MYC, BCL2 en/of BCL6 | | hooggradig B-cellymfoom met herschikking van MYC-, BCL2- en/of BCL6-gen
| | High grade B-cell lymphoma with MYC and BCL2 and/or BCL6 rearrangements | | A rare aggressive B-cell non-Hodgkin lymphoma with characteristics of rearrangement in MYC and BCL2 and/or BCL6 (so-called double-hit or triple-hit lymphoma). The category includes double-hit cases with features intermediate between diffuse large B-cell lymphoma (DLBCL) and Burkitt lymphoma, blastoid cases with a double-hit, and cases with a DLBCL not otherwise specified morphology with a double-hit. It refers only to de novo cases, not to lymphomas with a history of pre-existing or coexistent indolent lymphoma. Patients typically present with widespread disease, including involvement of lymph nodes, bone marrow and central nervous system. |
| | Id | 1172704005 | | Status | Defined |
| DHD Diagnosis thesaurus reference set |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | C85.1 | | Term | B-cel-lymfoom, niet gespecificeerd |
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| SNOMED CT to Orphanet simple map | 480541 |
| SNOMED CT to ICD-10 extended map | | Target | C85.7 | | Rule | TRUE | | Advice | ALWAYS C85.7 | POSSIBLE REQUIREMENT FOR ADDITIONAL CODE TO FULLY DESCRIBE DISEASE OR CONDITION | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | | Correlation | SNOMED CT source code to target map code correlation not specified |
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