niet-syndromale dextrocardie (aandoening)
niet-syndromale dextrocardie
Non syndromic dextrocardia
Non-syndromic dextrocardia
A rare, congenital, non-syndromic, developmental defect during embryogenesis with characteristics of positioning of the heart in the right hemithorax, with the base and apex of the heart pointing caudally and to the right, due to abnormalities of embryologic origin that are intrinsic to the heart itself. Situs inversus or situs solitus may be associated, with extracardiac visceral transposition anomalies usually present in the former case and additional cardiac defects (e.g. septal defects, transposition of the great arteries, double-outlet right ventricles, anomalous pulmonary venous return, tetralogy of Fallot) frequently observed in both cases.
Associated morphologycongenitale malpositie naar rechts
Finding sitegehele cor
Pathological processproces van pathologische ontwikkeling
SNOMED CT to Orphanet simple map1666
SNOMED CT to ICD-10 extended map
AdviceALWAYS Q24.0
CorrelationSNOMED CT source code to target map code correlation not specified