| intravasculair grootcellig B-cellymfoom (aandoening) | | intravasculair grootcellig B-cellymfoom | | Intravascular large B-cell lymphoma | | Malignant angioendotheliomatosis
Angioendotheliomatosis
Intravascular lymphomatosis
| | Intravascular large B-cell lymphoma (IVLBCL) is a very rare form of diffuse large B-cell lymphoma characterized by the selective growth of lymphoma cells within the lumina of small blood vessels (especially the capillaries) that most often presents with a wide range of clinical manifestations (as potentially any tissue can be involved), with patients from Western countries more frequently manifesting with neurological and cutaneous symptoms while patients from Asian countries more frequently displaying hepatosplenomegaly and thrombocytopenia. IVLBCL is characterized by an absence of lymphadenopathy, an aggressive clinical course and a poor prognosis. |
| | Id | 1157162007 | | Status | Defined |
| DHD Diagnosis thesaurus reference set |
| RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set | | Target | C83.8 | | Term | Non-folliculair lymfoom, overig |
| Target | M9680/3 | | Term | Diffuus grootcellig B-cellymfoom, NNO |
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| SNOMED CT to Orphanet simple map | 98839 |
| SNOMED CT to ICD-10 extended map | | Target | C83.8 | | Rule | TRUE | | Advice | ALWAYS C83.8 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE | | Correlation | SNOMED CT source code to target map code correlation not specified |
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