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dendritischecelsarcoom (aandoening)
dendritischecelsarcoom
sarcoom van dendritische cellen
Dendritic cell sarcoma
Sarcoma of dendritic cells
A rare dendritic cell tumor characterized by a neoplasm composed of spindled to ovoid cells with phenotypic features similar to those of normal indeterminate cells. The tumor cells consistently express S100 protein and CD1a, while langerin, specific B- and T-cell markers, CD30, the histiocytic marker CD163, and the follicular dendritic cell markers CD21, CD23, and CD35 are negative. Birbeck granules are absent on ultrastructural examination. Patients typically present with multiple papules, nodules, or plaques of the skin. Primary lymph node or splenic involvement is less common. Systemic symptoms are usually absent. The clinical course is highly variable.
Id1156495004
StatusDefined
Associated morphologydendritischecelsarcoom
DHD Diagnosis thesaurus reference set
ICD-10 complex map reference set
TargetC96.4
RuleTRUE
AdviceALWAYS C96.4 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE
CorrelationSNOMED CT source code to target map code correlation not specified