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acrokerato-elastoidosis (aandoening)
acrokerato-elastoidosis
Acrokeratoelastoidosis of Costa
Punctate palmoplantar hyperkeratosis type 3
Punctate palmoplantar keratoderma type 3
PPKP3 - palmoplantar keratoderma punctate type 3
Acrokerato-elastoidosis
A rare punctate palmoplantar keratoderma characterized by multiple small, round to oval or rhomboid, yellowish, hyperkeratotic papules and plaques most commonly localized to the palms of the hands and soles of the feet, potentially extending to the dorsum of the hands and feet in severe cases. Histopathological analysis shows hyperkeratosis, epidermal hypertrophy, and fragmentation and rarefaction of elastic fibers. The condition can be sporadic or familial.
Id111029001
StatusPrimitive
Associated morphologypapel
Finding sitestructuur van huid van manus
Associated morphologypapel
Finding sitestructuur van huid van voetzool
Associated morphologyhyperkeratose
Finding sitestructuur van huid van manus
Associated morphologyhyperkeratose
Finding sitestructuur van huid van voetzool
PALGA thesaurus simple reference set for pathology
DHD Diagnosis thesaurus reference set
RIVM authorized national diagnosis thesaurus to ICD10 complex mapping reference set
TargetQ82.8
TermOverige gespecificeerde congenitale misvormingen van huid
SNOMED CT to Orphanet simple map38
SNOMED CT to ICD-10 extended map
TargetL85.1
RuleTRUE
AdviceALWAYS L85.1
CorrelationSNOMED CT source code to target map code correlation not specified